内科理论与实践

内科理论与实践 >

2026 , Vol. 20 >Issue 06: 495 - 499

DOI: https://doi.org/10.16138/j.1673-6087.2025.06.12

综述

心脏淀粉样变性无创评估进展

  • 张茂森 ,
  • 车子刚 ,
  • 郭万华 ,
  • 钟业鸣 ,
  • 封成燕 ,
  • 魏旋
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  • 东南大学医学院附属南京同仁医院 a. 医学影像科；b. 核医学科，江苏 南京　211102
车子刚　E-mail：chezg@njtrh.org

收稿日期: 2024-09-04

  网络出版日期: 2026-01-30

基金资助

南京市卫生科技发展专项资金项目(YKK23263);东南大学医学院附属南京同仁医院院内科研项目(2023E003)

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《内科理论与实践》编辑部, 2025, 版权所有，未经授权，不得转载、摘编本刊文章，不得使用本刊的版式设计。
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Progress in noninvasive assessment of cardiac amyloidosis

  • ZHANG Maosen ,
  • CHE Zigang ,
  • GUO Wanhua ,
  • ZHONG Yeming ,
  • FENG Chengyan ,
  • WEI Xuan
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  • a. Department of Medical Imaging; b. Department of Nuclear Medicine, Nanjing Tongren Hospital, Southeast UniversitySchool of Medicine, Nanjing 211102, China

Received date: 2024-09-04

  Online published: 2026-01-30

Copyright

, 2025, Copyright reserved © 2025.
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摘要

淀粉样变性是由于蛋白质错误折叠和沉积导致人体重要组织器官功能受损的一组疾病。系统性淀粉样变性常累及心脏，是淀粉样变性患者的主要死因。心脏淀粉样变确诊困难、预后不佳，早期诊断及评估对患者的治疗及预后至关重要。本文将对几种无创诊断评估心脏淀粉样变技术进行阐述。

关键词： 心脏淀粉样变性; 心脏磁共振; 心电图; 超声心动图; 放射性核素显像

本文引用格式

张茂森 , 车子刚 , 郭万华 , 钟业鸣 , 封成燕 , 魏旋 . 心脏淀粉样变性无创评估进展[J]. 内科理论与实践, 2026 , 20(06) : 495 -499 . DOI: 10.16138/j.1673-6087.2025.06.12

Abstract

Amyloidosis is a group of disorders caused by misfolded proteins that deposit in tissues and impair the function of vital organs. Systemic amyloidosis frequently involves the heart and is a leading cause of death in affected patients. Cardiac amyloidosis is difficult to diagnose and carries a poor prognosis, making early diagnosis and assessment crucial for treatment and prognosis. This article reviews several noninvasive techniques for diagnosing and evaluating cardiac amyloidosis.

Key words： Cardiac amyloidosis; Cardiac magnetic resonance; Electrocardiogram; Echocardiography; Radionuclide imaging

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