先天性小耳畸形 , 　先天性泌尿生殖系统畸形 , 　发病率 , 　肾脏超声 , 　腹部 CT

Objective　To study the incidence of congenital urogenital malformations in patients with congenital microtia,

and to analyze the correlation between the two diseases. Methods　A retrospective analysis was performed on 3 143 patients

with microtia from January 2015 to December 2019, and the cases with genitourinary system malformations were counted

and classified through renal ultrasound or abdominal CT examination. The incidence of congenital microtia combined

with genitourinary system malformations and the side correlation between the affected ear and urogenital deformities were

analyzed. Results　Among 3 143 patients with congenital microtia, 163 cases were accompanied by congenital genitourinary

system malformations, including unilateral kidney deficiency, renal hypoplasia, hydronephrosis, hypospadias, and testicular

deformity, with a total incidence of 5.2%. Through data analysis, it can be seen that among the patients with congenital microtia

accompanied by congenital genitourinary malformation, the proportion of second-degree microtia was the highest, and the

proportion of hydronephrosis, renal cyst and testicular deformity was relatively high. What’s more, the side of congenital

microtia was associated with the side of congenital genitourinary malformations. Conclusion　In patients with congenital

microtia, the incidence of genitourinary malformation is higher than in the general population, and they both are more likely to be

ipsilateral. Such patients can be diagnosed through physical examination, renal ultrasound and abdominal CT, so as to focus on

renal function in subsequent treatment to improve the prognosis of these patients.

Congenital microtia, 　Congenital genitourinary malformation, 　Morbidity, 　Renal ultrasound, 　Abdominal CT