外科理论与实践

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2024 , Vol. 29 >Issue 02: 182 - 185

DOI: https://doi.org/10.16139/j.1007-9610.2024.02.15

综述

先天性胆管扩张症的病因、分型及诊断

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  • 中国医科大学附属盛京医院第二普通外科　胆道外科，辽宁 沈阳　110004
吴硕东，E-mail: wushuodong@aliyun.com

收稿日期: 2023-01-19

  网络出版日期: 2024-07-01

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Etiology, classification and diagnosis of congenital biliary dilatation

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  • The Second Department of General Surgery，Department of Biliary Surgery, Shengjing Hospital of China Medical University, Liaoning Shenyang 110004, China

Received date: 2023-01-19

  Online published: 2024-07-01

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摘要

先天性胆管扩张症（congenital biliary dilatation, CBD）的病因仍未明确，目前以胰胆管合流异常理论为主流。分型方面则以Todani分型应用最为广泛。另一方面，由董家鸿等提出的董氏分型对手术术式的选择也有着指导意义。CBD因为临床症状的特异性较差，发现及诊断较为困难，往往需要根据病史先做初步诊断，同时也相当依赖影像学检查的辅助，而血清学诊断因为方便和接受程度高的优势也对CBD的诊断起到关键的作用。本文就CBD的病因分型及诊断作一综述。

关键词： 先天性胆管扩张症; 先天性胆总管囊肿; 影像学诊断; 血清学诊断

本文引用格式

高振华, 吴硕东 . 先天性胆管扩张症的病因、分型及诊断[J]. 外科理论与实践, 2024 , 29(02) : 182 -185 . DOI: 10.16139/j.1007-9610.2024.02.15

Abstract

The etiology of congenital biliary dilatation (CBD) is still unclear. Currently, abnormal pancreatico-bile duct confluence is the mainstream theory. In terms of classification, Todani classification is the most widely used. On the other hand, Dong's classification which proposed by Dong Jiahong and his colleagues has guiding significance for the selection of surgical methods. CBD is difficult to detect and diagnose because of the poor specificity of clinical symptoms, and it is often necessary to make a preliminary diagnosis based on the medical history, and it is also quite dependent on the assistance of imaging. Serological examination also plays a key role in the diagnosis of CBD because of its convenience and high acceptance. This article reviewed the etiology, classification and diagnosis of CBD.

Key words： Congenital biliary dilatation(CBD); Congenital choledochal cyst; Imaging diagnosis; Serological diagnosis

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