The traditional transoral odontoidectomy is a complex and highly invasive surgery， primarily used for the treatment of spinal cord compression caused by congenital malformations， odontoid fractures， or other atlantoaxial pathologies. With the development of minimally invasive spinal techniques， full-endoscopic odontoidectomy has demonstrated significant advantages. In this study， a child with congenital odontoid malformation admitted in August 2024 was reported. The patient experienced numbness and weakness in all four limbs， inability to stand or walk independently， and was diagnosed with spinal cord compression caused by the odontoid malformation. After excluding contraindications， the patient underwent a successful transoral single-port endoscopic odontoidectomy. Intraoperative O-arm scans confirmed complete removal of the malformed odontoid and successful spinal cord decompression. The intraoperative blood loss was 10 mL， and the surgical incision was approximately 10 mm in length. No complications， such as neurological injury， were observed during surgery. This case report provides a detailed description of the technical aspects of this innovative transoral single-port endoscopic odontoidectomy， demonstrating its feasibility and potential advantages.

Cervical spine, Single-port endoscopic surgery, Odontoidectomy, Spinal decompression