Primary lymphedema is attributed to congenital developmental lymphoid abnormalities or dysfunction of the lymphatic system. There is relatively little research on primary lymphedema， and the treatment is mainly based on clinical practice guidelines for secondary lymphedema， including conservative treatment and surgical treatment. In this paper， the current status of surgical treatment for primary lymphedema in the limbs based on recent literature was reviewed.

Primary lymphedema, Surgical treatment, Lymphatic-venous anastomosis, Vascularized lymph node