原发性干燥综合征多学科诊疗专家共识（2024版）

doi:10.16138/j.1673-6087.2024.06.00

内科理论与实践

• 指南与共识 •

原发性干燥综合征多学科诊疗专家共识（2024版）

程昉^1a, 赵福涛^1a, 沈雪敏^1b, 李瑾^1c, 陈向军^2a, 王桂芳^2b, 李慧凛³, 薛鸾⁴, 齐军元⁵

1.上海交通大学医学院附属第九人民医院 a.风湿免疫科;b.口腔黏膜科;c.眼科,上海 200011;
2.复旦大学附属华山医院 a.神经内科;b.呼吸内科,上海 200040;
3.海军军医大学附属上海市浦东新区公利医院肾内科,上海 200135;
4.上海中医药大学附属岳阳中西医结合医院风湿免疫科,上海 200437;
5.中国医学科学院血液病医院血液内科,天津 300020

收稿日期:2024-11-27
通讯作者: 齐军元 E-mail：qijy@ihcams.ac.cn;赵福涛 E-mail：ftzhao@moisten.org

Expert consensus on multidisciplinary team diagnosis and treatment of primary Sjögren's syndrome (2024 edition)

CHENG Fang^1a, ZHAO Futao^1a, SHEN Xuemin^1b, LI Jin^1c, CHEN Xiangjun^2a, WANG Guifang^2b, LI Huilin³, XUE Luan⁴, QI Junyuan⁵

1. Shanghai Ninth People’s Hospital, Shanghai Jiao Tong University School of Medicine, a. Department of Rheumatology and Immunology; b. Department of Oral Medicine; c. Department of Ophthalmology, Shanghai 200011, China;
2. Huashan Hospital, Fudan University, a. Department of Neurology; b. Department of Respiratory Medicine, Shanghai 200040, China;
3. Department of Nephrology, Gongli Hospital of Shanghai Pudong New Area, Naval Military Medical University, Shanghai 200135, China;
4. Department of Rheumatology and Immunology, Yueyang Hospital of Integrated Traditional Chinese and Western Medicine, Shanghai University of Traditional Chinese Medicine, Shanghai 200437, China;
5. Department of Hematology, Blood Diseases Hospital, Chinese Academy of Medical Science, Tianjin 300020, China

Received:2024-11-27

摘要/Abstract

摘要： 原发性干燥综合征（primary Sjögren syndrome, PSS）是一种以外分泌腺和其他器官淋巴细胞浸润为特征的自身免疫性疾病。PSS临床表现异质性强,可出现不同程度的局部和系统受累,需通过多学科协作制定治疗方案。然而,目前我国缺乏统一的诊疗规范。多名相关学科专家基于国内外诊治经验和指南共识,通过名义群体法形成本共识,旨在为PSS患者的规范化诊疗提供指导和参考依据。

关键词: 干燥综合征, 多学科协作, 诊断, 治疗

Abstract: Primary Sjögren's syndrome (pSS) is an autoimmune disease characterized by lymphocytic infiltration of exocrine glands and other organs. pSS has strong clinical heterogeneity, with topical and systemic involvement with varying degrees of severity, and requires multidisciplinary collaboration to develop treatment strategies. However, there is currently no homogenous approach to the diagnosis and treatment of pSS in China. Experts from multiple related disciplines gave their opinions based on the evidence and guidelines from China and other countries, and agreement between them was achieved using the Nominal Group Technique, with the purpose of providing guidance for rational management of pSS patients.

Key words: Sjögren syndrome, Multiple-disciplinary team, Diagnosis, Treatment

中图分类号:

R593.2

程昉, 赵福涛, 沈雪敏, 李瑾, 陈向军, 王桂芳, 李慧凛, 薛鸾, 齐军元. 原发性干燥综合征多学科诊疗专家共识（2024版）[J]. 内科理论与实践, doi: 10.16138/j.1673-6087.2024.06.00.

CHENG Fang, ZHAO Futao, SHEN Xuemin, LI Jin, CHEN Xiangjun, WANG Guifang, LI Huilin, XUE Luan, QI Junyuan. Expert consensus on multidisciplinary team diagnosis and treatment of primary Sjögren's syndrome (2024 edition)[J]. Journal of Internal Medicine Concepts & Practice, doi: 10.16138/j.1673-6087.2024.06.00.

参考文献

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原发性干燥综合征多学科诊疗专家共识（2024版）

Expert consensus on multidisciplinary team diagnosis and treatment of primary Sjögren's syndrome (2024 edition)

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