原发性干燥综合征（primary Sjögren syndrome, PSS）是一种以外分泌腺和其他器官淋巴细胞浸润为特征的自身免疫性疾病。PSS临床表现异质性强,可出现不同程度的局部和系统受累,需通过多学科协作制定治疗方案。然而,目前我国缺乏统一的诊疗规范。多名相关学科专家基于国内外诊治经验和指南共识,通过名义群体法形成本共识,旨在为PSS患者的规范化诊疗提供指导和参考依据。
Primary Sjögren's syndrome (pSS) is an autoimmune disease characterized by lymphocytic infiltration of exocrine glands and other organs. pSS has strong clinical heterogeneity, with topical and systemic involvement with varying degrees of severity, and requires multidisciplinary collaboration to develop treatment strategies. However, there is currently no homogenous approach to the diagnosis and treatment of pSS in China. Experts from multiple related disciplines gave their opinions based on the evidence and guidelines from China and other countries, and agreement between them was achieved using the Nominal Group Technique, with the purpose of providing guidance for rational management of pSS patients.
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