Journal of Diagnostics Concepts & Practice ›› 2023, Vol. 22 ›› Issue (05): 460-465.doi: 10.16150/j.1671-2870.2023.05.007
• Original articles • Previous Articles Next Articles
FENG Li1a,2, REN Gang1a(), CAI Rong3(
), WANG Xinyun1a, WANG Hui2, ZHU Mingjie1b
Received:
2022-05-08
Online:
2023-10-25
Published:
2024-03-15
CLC Number:
FENG Li, REN Gang, CAI Rong, WANG Xinyun, WANG Hui, ZHU Mingjie. Clinical features study of perivascular epithelioid cell tumor (PEComa) in genitourinary system[J]. Journal of Diagnostics Concepts & Practice, 2023, 22(05): 460-465.
Table 1
Clinical and imaging findings of 5 cases of perivascular epithelioid cell tumor of genitourinary system
Serial numb-er | Gen-der | Age (years old) | Symptom | NSE | Location | Shape | Volume(mm) | Density | Necrosis | Enhancement type | Enhanced degree | Small blood vessels travel after enhanc-ement | Renal venous cancer thromb-us | Distant metastasis of tumor |
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
No.1 | male | sixty | No symptoms | high | Right kidney | Round | 9×7×8 | Homog-eneous | - | Fast in and out | Obvious | - | - | - |
No.2 | male | nine | Abdominal mass | high | Left kidney | Irregular | 150×160×190 | Heterog-eneous | + | Fast in and slow out | Medium | + | - | - |
No.3 | fema-le | sixty-one | No symptom | Norm-al | Right kidney | Oval | 100×161×190 | Heterog-eneous | - | Fast in and slow out | Medium | - | - | - |
No.4 | male | sixty-three | Ventosity | Norm-al | Left kidney | Irregular | 50×60×25 | Heterog-eneous | + | Fast in and slow out | Medium | + | - | - |
No.5 | fema-le | nine | Vaginal fluid | high | Vagina | Round | 21×17×25 | Homog-eneous | - | Enhancement appearances | Obvious | - | - | - |
Figure 1
PEComa in the right kidney (Case 1) 1a-1c: axial, a small nodular lesions in the right kidney grows outward with clear boundaries. CT value of plain scan is 46 HU, and CT values of the arterial and venous phases after enhancement are 101 HU and 76 HU respectively, showing fast in and out enhancement. 1a shows slightly high density on plain scan, 1b shows obvious enhancement in the arterial phase. 1c shows obvious decrease in venous phase and low density relatively. 1d-1h: a small nodular lesion of the right kidney growing outward, equal signal on T1WI and slightly low signal on T2WI, obviously enhancement in arterial phase, decreased enhancement in venous phase and delayed phase, showing relatively low signal.
Figure 2
PEComa in the left kidney (Case 2) 2a: axial, a large mixed density lesion of the left kidney is found in plain scan, with a low density area in the center and surrounding solid density. 2b: obvious enhancement of the surrounding solid part of the arterial phase, with vascular shadow visible inside, but no enhancement in the central low density area, and the lesion invading the psoas major and retroperitoneal space. 2b: the solid part of the focus in the venous phase continued to enhance significantly, but no enhancement was observed in the central low-density area. 2c-2d: the solid part of the focus in the delayed phase decreased in enhancement, but no enhancement was observed in the central low-density area.
Figure 3
PEComa in the vagina (Case 3) 3a: the right lateral wall of the lower vaginal segment was local thickening and distention in CT plain scan, and a small isodensity nodule was observed, with homogeneous density. 3b: obvious enhancement at arterial phase, 3c: decreased enhancement at venous phase.
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